Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis

Yıl: 2012 Cilt: 27 Sayı: 1 Sayfa Aralığı: 63 - 66 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis

Öz:
İmmunoglobulin G4 (IgG4) ilişkili sklerozan vaskülit, çeşitli organlarda yaygın IgG4-pozitif plazma hücreleri ve T-lenfosit infiltrasyonu ile karakterize bir hastalıktır. Serum IgG4 düzeyleri ve anti-IgG4 antikor immün boyamaları tanıda kullanışlıdır. Bu makalede, dispne, yaygın ödem ve göğüs ağrısı yakınmasıyla başvuran ve perikardiyal sıvı ve serum IgG4 düzeyinde artış görülen 61 yaşında bir erkek hasta sunuldu. Torakoabdominal bilgisayarlı tomografi (BT) taramasında aort arktan başlayan ve torakal ve abdominal aortu saran bir yumuşak doku kitlesi saptandı. Biyopsi yapıldıktan sonra, hastaya IgG4 ilişkili sklerozan vaskülit tanısı kondu.
Anahtar Kelime:

Konular: Romatoloji

İmmunoglobulin G4 İlişkili Sklerozan Vaskülitli Hastada Periaortitis, Koroner Vaskülit ve Retro-Orbital Pseudotümör Birlikteliği

Öz:
Immunoglobulin G4 (IgG4)-related sclerosing vasculitis is characterized by extensive IgG4-positive plasma cells and T-lymphocyte infiltration of various organs. Serum IgG4 level and immunostaining with anti-IgG4 antibody are useful for the diagnosis. In this article, a 61-year-old male patient who was admitted with the complaints of dyspnea, diffuse edema and chest pain and presented with increased pericardial fluid and serum IgG4 level was reported. Thoracoabdominal computed tomography (CT) scan demonstrated a soft tissue mass starting at arcus aorta and surrounding thoracal and abdominal aorta. After biopsy was obtained, the patient was diagnosed with IgG4-related sclerosing vasculitis.
Anahtar Kelime:

Konular: Romatoloji
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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APA BİLGİN B, YEŞİLKAYA Y, TÜRKER B, VARAN Ö, Aydın Ö, Işık M, Kılıç L, DOĞAN İ, bolayır b, KİRAZ S, ATALAR E, CENGİZ M (2012). Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. , 63 - 66.
Chicago BİLGİN Burak,YEŞİLKAYA Yakup,TÜRKER Burcu,VARAN Özkan,Aydın Öznur,Işık Metin,Kılıç Levent,DOĞAN İsmail,bolayır başak,KİRAZ Sedat,ATALAR Enver,CENGİZ Mustafa Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. (2012): 63 - 66.
MLA BİLGİN Burak,YEŞİLKAYA Yakup,TÜRKER Burcu,VARAN Özkan,Aydın Öznur,Işık Metin,Kılıç Levent,DOĞAN İsmail,bolayır başak,KİRAZ Sedat,ATALAR Enver,CENGİZ Mustafa Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. , 2012, ss.63 - 66.
AMA BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. . 2012; 63 - 66.
Vancouver BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. . 2012; 63 - 66.
IEEE BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M "Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis." , ss.63 - 66, 2012.
ISNAD BİLGİN, Burak vd. "Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis". (2012), 63-66.
APA BİLGİN B, YEŞİLKAYA Y, TÜRKER B, VARAN Ö, Aydın Ö, Işık M, Kılıç L, DOĞAN İ, bolayır b, KİRAZ S, ATALAR E, CENGİZ M (2012). Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. Turkish Journal of Rheumatology(.)Archives of Rheumatology, 27(1), 63 - 66.
Chicago BİLGİN Burak,YEŞİLKAYA Yakup,TÜRKER Burcu,VARAN Özkan,Aydın Öznur,Işık Metin,Kılıç Levent,DOĞAN İsmail,bolayır başak,KİRAZ Sedat,ATALAR Enver,CENGİZ Mustafa Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. Turkish Journal of Rheumatology(.)Archives of Rheumatology 27, no.1 (2012): 63 - 66.
MLA BİLGİN Burak,YEŞİLKAYA Yakup,TÜRKER Burcu,VARAN Özkan,Aydın Öznur,Işık Metin,Kılıç Levent,DOĞAN İsmail,bolayır başak,KİRAZ Sedat,ATALAR Enver,CENGİZ Mustafa Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. Turkish Journal of Rheumatology(.)Archives of Rheumatology, vol.27, no.1, 2012, ss.63 - 66.
AMA BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. Turkish Journal of Rheumatology(.)Archives of Rheumatology. 2012; 27(1): 63 - 66.
Vancouver BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis. Turkish Journal of Rheumatology(.)Archives of Rheumatology. 2012; 27(1): 63 - 66.
IEEE BİLGİN B,YEŞİLKAYA Y,TÜRKER B,VARAN Ö,Aydın Ö,Işık M,Kılıç L,DOĞAN İ,bolayır b,KİRAZ S,ATALAR E,CENGİZ M "Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis." Turkish Journal of Rheumatology(.)Archives of Rheumatology, 27, ss.63 - 66, 2012.
ISNAD BİLGİN, Burak vd. "Periaortitis, Coronary Vasculitis and Retro-Orbital Pseudotumor in a Patient with Immunoglobulin G4-Related Sclerosing Vasculitis". Turkish Journal of Rheumatology(.)Archives of Rheumatology 27/1 (2012), 63-66.