Primitive neuroectodermal tumor in a child with Currarino syndrome

yavuz, gökçe; Ozcan, Rahsan; CELKAN, TÜLIN TIRAJE; YILMAZ, GIZEM; comunoglu, nil; ocak, suheyla; ÇEBİ, MEMNUNE NUR

doi:10.24953/turkjped.2021.264

Primitive neuroectodermal tumor in a child with Currarino syndrome

Memnune Nur CEBİ, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Pediatrik Hematoloji ve Onkoloji Anabilim Dalı, İstanbul, Türkiye)

GIZEM YILMAZ, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Pediatrik Hematoloji ve Onkoloji Anabilim Dalı, İstanbul, Türkiye)

gökçe yavuz, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Çocuk Cerrahisi Anabilim Dalı, İstanbul, Türkiye)

Rahşan ÖZCAN, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Çocuk Cerrahisi Anabilim Dalı, İstanbul, Türkiye)

Süheyla OCAK, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Pediatrik Hematoloji ve Onkoloji Anabilim Dalı, İstanbul, Türkiye)

Tiraje CELKAN, (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Pediatrik Hematoloji ve Onkoloji Anabilim Dalı, İstanbul, Türkiye)

Nil ÇOMUNOĞLU (İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Patoloji Anabilim Dalı, İstanbul, Türkiye)

Turkish Journal of Pediatrics

1 0

Yıl: 2022 Cilt: 64 Sayı: 2 Sayfa Aralığı: 385 - 388 Metin Dili: İngilizce DOI: 10.24953/turkjped.2021.264 İndeks Tarihi: 15-12-2022

Primitive neuroectodermal tumor in a child with Currarino syndrome

Öz:

Background. Curarino syndrome is a rare and complex anomaly with the triad of anorectal malformation, presacral mass and sacral bone deformation. The most common cause of the presacral mass is meningioma, but teratoma is the diagnosis in about one-third of the cases. Malignant transformation of teratoma in the form of carcinoma, rhabdomyosarcoma and leukemia have previously been reported on rare occasions. Case. A 19 month-old-girl was referred with a presacral mass of 29mm x 23mm x 24mm. She was diagnosed as Currarino syndrome. The presacral mass was surgically resected and pathological examination revealed a foci of primitive neurectodermal tumor. Conclusions. This is the first case of Currarino syndrome with a primitive neuroectodermal tumor (PNET) foci in the presacral mass. Considering the risk of malignant transformation, the accurate pathological examination is important for complete systemic evaluation and treatment plan in these children.

Anahtar Kelime:

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	ÇEBİ M, YILMAZ G, yavuz g, Ozcan R, ocak s, CELKAN T, comunoglu n (2022). Primitive neuroectodermal tumor in a child with Currarino syndrome. , 385 - 388. 10.24953/turkjped.2021.264
Chicago	ÇEBİ MEMNUNE NUR,YILMAZ GIZEM,yavuz gökçe,Ozcan Rahsan,ocak suheyla,CELKAN TÜLIN TIRAJE,comunoglu nil Primitive neuroectodermal tumor in a child with Currarino syndrome. (2022): 385 - 388. 10.24953/turkjped.2021.264
MLA	ÇEBİ MEMNUNE NUR,YILMAZ GIZEM,yavuz gökçe,Ozcan Rahsan,ocak suheyla,CELKAN TÜLIN TIRAJE,comunoglu nil Primitive neuroectodermal tumor in a child with Currarino syndrome. , 2022, ss.385 - 388. 10.24953/turkjped.2021.264
AMA	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n Primitive neuroectodermal tumor in a child with Currarino syndrome. . 2022; 385 - 388. 10.24953/turkjped.2021.264
Vancouver	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n Primitive neuroectodermal tumor in a child with Currarino syndrome. . 2022; 385 - 388. 10.24953/turkjped.2021.264
IEEE	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n "Primitive neuroectodermal tumor in a child with Currarino syndrome." , ss.385 - 388, 2022. 10.24953/turkjped.2021.264
ISNAD	ÇEBİ, MEMNUNE NUR vd. "Primitive neuroectodermal tumor in a child with Currarino syndrome". (2022), 385-388. https://doi.org/10.24953/turkjped.2021.264

APA	ÇEBİ M, YILMAZ G, yavuz g, Ozcan R, ocak s, CELKAN T, comunoglu n (2022). Primitive neuroectodermal tumor in a child with Currarino syndrome. Turkish Journal of Pediatrics, 64(2), 385 - 388. 10.24953/turkjped.2021.264
Chicago	ÇEBİ MEMNUNE NUR,YILMAZ GIZEM,yavuz gökçe,Ozcan Rahsan,ocak suheyla,CELKAN TÜLIN TIRAJE,comunoglu nil Primitive neuroectodermal tumor in a child with Currarino syndrome. Turkish Journal of Pediatrics 64, no.2 (2022): 385 - 388. 10.24953/turkjped.2021.264
MLA	ÇEBİ MEMNUNE NUR,YILMAZ GIZEM,yavuz gökçe,Ozcan Rahsan,ocak suheyla,CELKAN TÜLIN TIRAJE,comunoglu nil Primitive neuroectodermal tumor in a child with Currarino syndrome. Turkish Journal of Pediatrics, vol.64, no.2, 2022, ss.385 - 388. 10.24953/turkjped.2021.264
AMA	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n Primitive neuroectodermal tumor in a child with Currarino syndrome. Turkish Journal of Pediatrics. 2022; 64(2): 385 - 388. 10.24953/turkjped.2021.264
Vancouver	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n Primitive neuroectodermal tumor in a child with Currarino syndrome. Turkish Journal of Pediatrics. 2022; 64(2): 385 - 388. 10.24953/turkjped.2021.264
IEEE	ÇEBİ M,YILMAZ G,yavuz g,Ozcan R,ocak s,CELKAN T,comunoglu n "Primitive neuroectodermal tumor in a child with Currarino syndrome." Turkish Journal of Pediatrics, 64, ss.385 - 388, 2022. 10.24953/turkjped.2021.264
ISNAD	ÇEBİ, MEMNUNE NUR vd. "Primitive neuroectodermal tumor in a child with Currarino syndrome". Turkish Journal of Pediatrics 64/2 (2022), 385-388. https://doi.org/10.24953/turkjped.2021.264