TY  - JOUR
TI  - Primitive neuroectodermal tumor in a child with Currarino syndrome
AB  - Background. Curarino syndrome is a rare and complex anomaly with the triad of anorectal malformation, presacral mass and sacral bone deformation. The most common cause of the presacral mass is meningioma, but teratoma is the diagnosis in about one-third of the cases. Malignant transformation of teratoma in the form of carcinoma, rhabdomyosarcoma and leukemia have previously been reported on rare occasions. Case. A 19 month-old-girl was referred with a presacral mass of 29mm x 23mm x 24mm. She was diagnosed as Currarino syndrome. The presacral mass was surgically resected and pathological examination revealed a foci of primitive neurectodermal tumor. Conclusions. This is the first case of Currarino syndrome with a primitive neuroectodermal tumor (PNET) foci in the presacral mass. Considering the risk of malignant transformation, the accurate pathological examination is important for complete systemic evaluation and treatment plan in these children.
AU  - yavuz, gökçe
AU  - Ozcan, Rahsan
AU  - CELKAN, TÜLIN TIRAJE
AU  - YILMAZ, GIZEM
AU  - comunoglu, nil
AU  - ocak, suheyla
AU  - ÇEBİ, MEMNUNE NUR
DO  - 10.24953/turkjped.2021.264
PY  - 2022
JO  - Turkish Journal of Pediatrics
VL  - 64
IS  - 2
SN  - 0041-4301
SP  - 385
EP  - 388
DB  - TRDizin
UR  - http://search/yayin/detay/1138660
ER  -