A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major
Yıl: 2023 Cilt: 3 Sayı: 1 Sayfa Aralığı: 43 - 47 Metin Dili: İngilizce DOI: 10.4274/MNM.2022.22124 İndeks Tarihi: 11-05-2023
A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major
Öz: Thalassemia is an inherited hematologic disease in which the body makes an abnormal form of hemoglobin. Patients are diagnosed with thalassemia major due to severe anemia and clinical symptoms. Thalassemia major is a common disease in the Turkish Republic of Northern Cyprus (TRNC) and other Mediterranean countries. Thalassemia major is a chronic and severe health problem. Thalassemia major damages organs due to intense iron accumulation and deep anemia. It negatively affects the quality of life and shortens life. Also, due to chronic disease, patients experience psychological and social problems. In this review, we present thalassemia major in the TRNC. The rate of patients has decreased with prevention programs and no sick baby has been born after 2001 in the TRNC. However, existing thalassemia patients have many physical and psychosocial problems and the treatment processes the patients are challenging. Since TRNC is an island that receives immigration, it has a sociological texture that includes different cultures, which can increase the dimensions of this problem. Therefore, this review focuses on the thalassemia process and the psychosocial problems caused by the disease in the TRNC.
Anahtar Kelime: Kuzey Kıbrıs Türk Cumhuriyeti’nde Bir Hematolojik Hastalık: Talasemi Majör
Öz: alasemi, vücudun anormal bir hemoglobin formu oluşturduğu kalıtsal bir hematolojik hastalıktır. Hastalara şiddetli anemi ve klinik semptomlar nedeniyle talasemi majör tanısı konur. Talasemi majör, Kuzey Kıbrıs Türk Cumhuriyeti (KKTC) ve diğer Akdeniz ülkelerinde yaygın olarak görülen bir hastalıktır. Talasemi majör, kronik ve ciddi bir sağlık sorunudur. Talasemi majör, yoğun demir birikimi ve derin anemi nedeniyle organlara zarar verir. Yaşam kalitesini olumsuz etkiler ve ömrü kısaltır. Ayrıca kronik hastalık nedeniyle hastalar psikolojik ve sosyal sorunlar yaşamaktadır. Bu derlemede KKTC’deki talasemi majörü sunuyoruz. Önleme programları ile hasta oranı düşmüş ve 2001 yılından sonra KKTC’de hasta bebek dünyaya gelmemiştir. Ancak mevcut talasemi hastalarının birçok fiziksel ve psikososyal sorunu bulunmakta ve tedavi süreçleri hastaları zorlamaktadır. KKTC göç alan bir ada olması nedeniyle farklı kültürleri içinde barındıran sosyolojik bir dokuya sahip olması bu sorunun boyutlarını artırabilmektedir. Bu nedenle bu derleme, KKTC’de talasemi sürecine ve hastalığın yol açtığı psikososyal sorunlara odaklanmaktadır.
Anahtar Kelime: Belge Türü: Makale Makale Türü: Derleme Erişim Türü: Erişime Açık
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| APA | ŞAHİN TARIM H, Öz F (2023). A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. , 43 - 47. 10.4274/MNM.2022.22124 |
| Chicago | ŞAHİN TARIM HAZEL,Öz Fatma A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. (2023): 43 - 47. 10.4274/MNM.2022.22124 |
| MLA | ŞAHİN TARIM HAZEL,Öz Fatma A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. , 2023, ss.43 - 47. 10.4274/MNM.2022.22124 |
| AMA | ŞAHİN TARIM H,Öz F A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. . 2023; 43 - 47. 10.4274/MNM.2022.22124 |
| Vancouver | ŞAHİN TARIM H,Öz F A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. . 2023; 43 - 47. 10.4274/MNM.2022.22124 |
| IEEE | ŞAHİN TARIM H,Öz F "A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major." , ss.43 - 47, 2023. 10.4274/MNM.2022.22124 |
| ISNAD | ŞAHİN TARIM, HAZEL - Öz, Fatma. "A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major". (2023), 43-47. https://doi.org/10.4274/MNM.2022.22124 |
| APA | ŞAHİN TARIM H, Öz F (2023). A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. Mediterranean nursing and midwifery (Online), 3(1), 43 - 47. 10.4274/MNM.2022.22124 |
| Chicago | ŞAHİN TARIM HAZEL,Öz Fatma A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. Mediterranean nursing and midwifery (Online) 3, no.1 (2023): 43 - 47. 10.4274/MNM.2022.22124 |
| MLA | ŞAHİN TARIM HAZEL,Öz Fatma A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. Mediterranean nursing and midwifery (Online), vol.3, no.1, 2023, ss.43 - 47. 10.4274/MNM.2022.22124 |
| AMA | ŞAHİN TARIM H,Öz F A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. Mediterranean nursing and midwifery (Online). 2023; 3(1): 43 - 47. 10.4274/MNM.2022.22124 |
| Vancouver | ŞAHİN TARIM H,Öz F A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major. Mediterranean nursing and midwifery (Online). 2023; 3(1): 43 - 47. 10.4274/MNM.2022.22124 |
| IEEE | ŞAHİN TARIM H,Öz F "A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major." Mediterranean nursing and midwifery (Online), 3, ss.43 - 47, 2023. 10.4274/MNM.2022.22124 |
| ISNAD | ŞAHİN TARIM, HAZEL - Öz, Fatma. "A Hematologic Disease in the Turkish Republic of Northern Cyprus: Thalassemia Major". Mediterranean nursing and midwifery (Online) 3/1 (2023), 43-47. https://doi.org/10.4274/MNM.2022.22124 |
