Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience

AKBAŞ, TOLGA; Erdem, Sevcan; Subaşı, Berivan; Varan, Celal; Özbarlas, Nazan; demir, Fadli; salih, orhan kemal

doi:10.5606/tgkdc.dergisi.2023.23396

Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience

Fadli DEMİR, (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Tolga AKBAŞ, (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Sevcan ERDEM, (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Berivan SUBAŞI, (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Celal VARAN, (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Orhan Kemal SALİH, (Çukurova Üniversitesi, Tıp Fakültesi, Kalp Damar Cerrahisi Anabilim Dalı, Çocuk Kalp Cerrahisi Anabilim Dalı, Adana, Türkiye)

Nazan ÖZBARLAS (Çukurova Üniversitesi, Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Kardiyolojisi Anabilim Dalı, Adana, Türkiye)

Türk Göğüs Kalp Damar Cerrahisi Dergisi

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Yıl: 2023 Cilt: 31 Sayı: 1 Sayfa Aralığı: 19 - 28 Metin Dili: İngilizce DOI: 10.5606/tgkdc.dergisi.2023.23396 İndeks Tarihi: 30-05-2023

Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience

Öz:

Background: The aim of the study was to evaluate the clinical and diagnostic findings, treatment, and follow-up of cases of anomalous origin of coronary arteries from the pulmonary artery. Methods: Between January 1998 and June 2021, a total of 14 patients (5 males, 9 females; median age: 15 months; range, 3 to 156 months) diagnosed with anomalous origin of coronary arteries from the pulmonary artery were retrospectively analyzed. Demographic and clinical data of the patients, electrocardiographic, echocardiographic, angiographic, surgical, and follow-up findings were evaluated. Results: The most common symptoms were respiratory distress (n=6) and murmur (n=3). With the exception of three cases, all other patients were diagnosed by echocardiography in the first examination. Severe mitral valve insufficiency was detected in four patients and four other patients had moderate mitral insufficiency on echocardiography. Ejection fraction values ranged between 38 and 79%. Eleven patients underwent direct implantation of the coronary artery into the aorta, and three underwent a Takeuchi procedure. Mortality occurred in only one case. After surgery, mitral insufficiency and ejection fraction values improved. Median follow-up was 62 (range, 5 to 170) months and all patients were asymptomatic, except one who required redo surgery. Conclusion: Anomalous origin of the coronary arteries from the pulmonary artery is an uncommon congenital anomaly. Echocardiography is the main diagnostic tool. If all echocardiographic findings of the coronary anomaly are not investigated thoroughly, the diagnosis may be overlooked

Anahtar Kelime:

Pulmoner arterden çıkan koroner arter anomalisi: Tek merkez deneyimi

Öz:

Amaç: Bu çalışmada pulmoner arterden çıkan koroner arter anomalisi olan olguların klinik ve tanısal bulguları, tedavi ve takipleri değerlendirildi. Ça lışma planı: Ocak 1998 - Haziran 2021 tarihleri arasında pulmoner arterden çıkan koroner arter anomalisi tanısı olan toplam 14 hasta (5 erkek, 9 kız; medyan yaş: 15 ay; dağılım, 3-156 ay) retrospektif olarak incelendi. Hastaların demografik ve klinik verileri, elektrokardiyografik, ekokardiyografik, anjiyografik, cerrahi ve takip bulguları incelendi. Bulgular: En sık görülen semptom solunum sıkıntısı (n=6) ve üfürüm idi (n=3). Üç hasta haricinde geri kalan hastalara ilk değerlendirmede ekokardiyografi ile tanı konuldu. Ekokardiyografide dört hastada ciddi ve diğer dört hastada orta derecede mitral yetersizlik tespit edildi. Ejeksiyon fraksiyonu %38 ila %79 aralığında idi. On bir hastaya koroner arterin aorta direkt reimplantasyonu, üçüne ise Takeuchi ameliyatı yapıldı. Yalnızca bir hastada mortalite izlendi. Ameliyat sonrası mitral yetersizlik ve ejeksiyon fraksiyon değerlerinde düzelme görüldü. Medyan takip süresi 62 (dağılım, 5-170) ay olup, tekrar ameliyat gereken bir hasta haricinde hastaların tümü asemptomatik idi. So nuç:Pulmoner arterden çıkan koroner arter anomalileri nadir görülen doğumsal anomalilerdir. Ekokardiyografi temel tanı aracıdır. Tüm ekokardiyografik bulgular dikkatli bir şekilde araştırılmaz ise, tanı kolaylıkla gözden kaçabilir.

Anahtar Kelime:

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

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APA	demir F, AKBAŞ T, Erdem S, Subaşı B, Varan C, salih o, Özbarlas N (2023). Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. , 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
Chicago	demir Fadli,AKBAŞ TOLGA,Erdem Sevcan,Subaşı Berivan,Varan Celal,salih orhan kemal,Özbarlas Nazan Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. (2023): 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
MLA	demir Fadli,AKBAŞ TOLGA,Erdem Sevcan,Subaşı Berivan,Varan Celal,salih orhan kemal,Özbarlas Nazan Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. , 2023, ss.19 - 28. 10.5606/tgkdc.dergisi.2023.23396
AMA	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. . 2023; 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
Vancouver	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. . 2023; 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
IEEE	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N "Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience." , ss.19 - 28, 2023. 10.5606/tgkdc.dergisi.2023.23396
ISNAD	demir, Fadli vd. "Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience". (2023), 19-28. https://doi.org/10.5606/tgkdc.dergisi.2023.23396

APA	demir F, AKBAŞ T, Erdem S, Subaşı B, Varan C, salih o, Özbarlas N (2023). Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. Türk Göğüs Kalp Damar Cerrahisi Dergisi, 31(1), 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
Chicago	demir Fadli,AKBAŞ TOLGA,Erdem Sevcan,Subaşı Berivan,Varan Celal,salih orhan kemal,Özbarlas Nazan Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. Türk Göğüs Kalp Damar Cerrahisi Dergisi 31, no.1 (2023): 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
MLA	demir Fadli,AKBAŞ TOLGA,Erdem Sevcan,Subaşı Berivan,Varan Celal,salih orhan kemal,Özbarlas Nazan Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. Türk Göğüs Kalp Damar Cerrahisi Dergisi, vol.31, no.1, 2023, ss.19 - 28. 10.5606/tgkdc.dergisi.2023.23396
AMA	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. Türk Göğüs Kalp Damar Cerrahisi Dergisi. 2023; 31(1): 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
Vancouver	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience. Türk Göğüs Kalp Damar Cerrahisi Dergisi. 2023; 31(1): 19 - 28. 10.5606/tgkdc.dergisi.2023.23396
IEEE	demir F,AKBAŞ T,Erdem S,Subaşı B,Varan C,salih o,Özbarlas N "Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience." Türk Göğüs Kalp Damar Cerrahisi Dergisi, 31, ss.19 - 28, 2023. 10.5606/tgkdc.dergisi.2023.23396
ISNAD	demir, Fadli vd. "Anomalous origin of coronary arteries from the pulmonary artery: A single-center experience". Türk Göğüs Kalp Damar Cerrahisi Dergisi 31/1 (2023), 19-28. https://doi.org/10.5606/tgkdc.dergisi.2023.23396