Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data

Background. We aimed to determine the number of cystic fibrosis (CF) patients recorded in the Cystic Fibrosis Registry of Türkiye (CFRT) who were in need of lung transplantation (LT) referral and examine clinical differences between patients who were LT candidates due to rapid forced expiratory volume in one second (FEV₁) decline and LT candidates without rapid FEV₁ decline in the last year to identify a preventable cause in patients with such rapid FEV₁ decline. Methods. All CF patients recorded in the CFRT in 2018 were evaluated in terms of LT. Patients were divided into those with FEV₁ below 50% and in need of LT due to a decrease of 20% or more in the previous year (Group 1) and those who did not have FEV₁ decline of more than 20% in the previous year but had other indications for LT (Group 2). Demographic and clinical features were compared between the two groups. Results. Of 1488 patients registered in CFRT, 58 had a need for LT. Twenty patients were included in Group 1 and others in Group 2. Our findings did not reveal any significant variations in treatment, chronic infection status, or complications between the two groups. The average weight z-score was significantly higher in Group 1. Positive correlations were detected between weight z-score and FEV₁ in 2017 in Group 1 and between FEV₁ values in 2017 and 2018 in Group 2. Conclusions. There appears to be a relationship between the nutritional status and weight z-scores of CF patients and pulmonary function, which may indirectly affect the need for lung transplantation referral.

Anahtar Kelime: cystic fibrosis lung transplantation registry

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

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APA	Onay Z, Sismanlar Eyuboglu T, Aslan A, Ramasli Gursoy T, Yalcin E, Kiper N, Emiralioglu N, Selimoğlu Şen H, ŞEN v, ünal G, YILMAZ A, Kilinc A, cokugras H, Kilic Baskan A, Yazan H, Çollak A, Uzuner S, Sasihuseyinoglu A, ÖZCAN D, Altintas D, Kartal Öztürk G, Demir E, Bingöl A, BAŞARAN E, Cekic S, Sapan N, Irmak I, Damadoglu E, Tuğcu G, Eryilmaz Polat S, Özdemir A, harmancı k, KILIÇ G, Hangul M, Kose M, TAMAY Z, Yuksel H, ÖZCAN G, topal e, Can D, Korkmaz P, Çaltepe G, KILIÇ M, Ozdogan S, CAKIR E, ÇOBANOGLU N, PEKCAN S, CINEL G, ÖZÇELİK U, Dogru D (2023). Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. , 257 - 268. 10.24953/turkjped.2021.4930
Chicago	Onay Zeynep Reyhan,Sismanlar Eyuboglu Tugba,Aslan Ayse Tana,Ramasli Gursoy Tugba,Yalcin Ebru,Kiper Nural,Emiralioglu Nagehan,Selimoğlu Şen Hadice,ŞEN velat,ünal Gökçen,YILMAZ Asli imran,Kilinc Ayse Ayzit,cokugras Haluk Cezmi,Kilic Baskan Azer,Yazan Hakan,Çollak Abdulhamit,Uzuner Selcuk,Sasihuseyinoglu Ayse Senay,ÖZCAN Dilek,Altintas Derya Ufuk,Kartal Öztürk Gökçen,Demir Esen,Bingöl Ayşen,BAŞARAN ERDEM,Cekic Sukru,Sapan Nihat,Irmak Ilim,Damadoglu Ebru,Tuğcu Gökçen Dilşa,Eryilmaz Polat Sanem,Özdemir Ali,harmancı koray,KILIÇ Gonca,Hangul Melih,Kose Mehmet Alp,TAMAY ZEYNEP ÜLKER,Yuksel Hasan,ÖZCAN Gizem,topal erdem,Can Demet,Korkmaz Pervin,Çaltepe Gönül,KILIÇ Mehmet,Ozdogan Sebnem,CAKIR Erkan,ÇOBANOGLU NAZAN,PEKCAN SEVGI,CINEL GUZIN,ÖZÇELİK UĞUR,Dogru Deniz Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. (2023): 257 - 268. 10.24953/turkjped.2021.4930
MLA	Onay Zeynep Reyhan,Sismanlar Eyuboglu Tugba,Aslan Ayse Tana,Ramasli Gursoy Tugba,Yalcin Ebru,Kiper Nural,Emiralioglu Nagehan,Selimoğlu Şen Hadice,ŞEN velat,ünal Gökçen,YILMAZ Asli imran,Kilinc Ayse Ayzit,cokugras Haluk Cezmi,Kilic Baskan Azer,Yazan Hakan,Çollak Abdulhamit,Uzuner Selcuk,Sasihuseyinoglu Ayse Senay,ÖZCAN Dilek,Altintas Derya Ufuk,Kartal Öztürk Gökçen,Demir Esen,Bingöl Ayşen,BAŞARAN ERDEM,Cekic Sukru,Sapan Nihat,Irmak Ilim,Damadoglu Ebru,Tuğcu Gökçen Dilşa,Eryilmaz Polat Sanem,Özdemir Ali,harmancı koray,KILIÇ Gonca,Hangul Melih,Kose Mehmet Alp,TAMAY ZEYNEP ÜLKER,Yuksel Hasan,ÖZCAN Gizem,topal erdem,Can Demet,Korkmaz Pervin,Çaltepe Gönül,KILIÇ Mehmet,Ozdogan Sebnem,CAKIR Erkan,ÇOBANOGLU NAZAN,PEKCAN SEVGI,CINEL GUZIN,ÖZÇELİK UĞUR,Dogru Deniz Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. , 2023, ss.257 - 268. 10.24953/turkjped.2021.4930
AMA	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. . 2023; 257 - 268. 10.24953/turkjped.2021.4930
Vancouver	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. . 2023; 257 - 268. 10.24953/turkjped.2021.4930
IEEE	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D "Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data." , ss.257 - 268, 2023. 10.24953/turkjped.2021.4930
ISNAD	Onay, Zeynep Reyhan vd. "Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data". (2023), 257-268. https://doi.org/10.24953/turkjped.2021.4930

APA	Onay Z, Sismanlar Eyuboglu T, Aslan A, Ramasli Gursoy T, Yalcin E, Kiper N, Emiralioglu N, Selimoğlu Şen H, ŞEN v, ünal G, YILMAZ A, Kilinc A, cokugras H, Kilic Baskan A, Yazan H, Çollak A, Uzuner S, Sasihuseyinoglu A, ÖZCAN D, Altintas D, Kartal Öztürk G, Demir E, Bingöl A, BAŞARAN E, Cekic S, Sapan N, Irmak I, Damadoglu E, Tuğcu G, Eryilmaz Polat S, Özdemir A, harmancı k, KILIÇ G, Hangul M, Kose M, TAMAY Z, Yuksel H, ÖZCAN G, topal e, Can D, Korkmaz P, Çaltepe G, KILIÇ M, Ozdogan S, CAKIR E, ÇOBANOGLU N, PEKCAN S, CINEL G, ÖZÇELİK U, Dogru D (2023). Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. Turkish Journal of Pediatrics, 65(2), 257 - 268. 10.24953/turkjped.2021.4930
Chicago	Onay Zeynep Reyhan,Sismanlar Eyuboglu Tugba,Aslan Ayse Tana,Ramasli Gursoy Tugba,Yalcin Ebru,Kiper Nural,Emiralioglu Nagehan,Selimoğlu Şen Hadice,ŞEN velat,ünal Gökçen,YILMAZ Asli imran,Kilinc Ayse Ayzit,cokugras Haluk Cezmi,Kilic Baskan Azer,Yazan Hakan,Çollak Abdulhamit,Uzuner Selcuk,Sasihuseyinoglu Ayse Senay,ÖZCAN Dilek,Altintas Derya Ufuk,Kartal Öztürk Gökçen,Demir Esen,Bingöl Ayşen,BAŞARAN ERDEM,Cekic Sukru,Sapan Nihat,Irmak Ilim,Damadoglu Ebru,Tuğcu Gökçen Dilşa,Eryilmaz Polat Sanem,Özdemir Ali,harmancı koray,KILIÇ Gonca,Hangul Melih,Kose Mehmet Alp,TAMAY ZEYNEP ÜLKER,Yuksel Hasan,ÖZCAN Gizem,topal erdem,Can Demet,Korkmaz Pervin,Çaltepe Gönül,KILIÇ Mehmet,Ozdogan Sebnem,CAKIR Erkan,ÇOBANOGLU NAZAN,PEKCAN SEVGI,CINEL GUZIN,ÖZÇELİK UĞUR,Dogru Deniz Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. Turkish Journal of Pediatrics 65, no.2 (2023): 257 - 268. 10.24953/turkjped.2021.4930
MLA	Onay Zeynep Reyhan,Sismanlar Eyuboglu Tugba,Aslan Ayse Tana,Ramasli Gursoy Tugba,Yalcin Ebru,Kiper Nural,Emiralioglu Nagehan,Selimoğlu Şen Hadice,ŞEN velat,ünal Gökçen,YILMAZ Asli imran,Kilinc Ayse Ayzit,cokugras Haluk Cezmi,Kilic Baskan Azer,Yazan Hakan,Çollak Abdulhamit,Uzuner Selcuk,Sasihuseyinoglu Ayse Senay,ÖZCAN Dilek,Altintas Derya Ufuk,Kartal Öztürk Gökçen,Demir Esen,Bingöl Ayşen,BAŞARAN ERDEM,Cekic Sukru,Sapan Nihat,Irmak Ilim,Damadoglu Ebru,Tuğcu Gökçen Dilşa,Eryilmaz Polat Sanem,Özdemir Ali,harmancı koray,KILIÇ Gonca,Hangul Melih,Kose Mehmet Alp,TAMAY ZEYNEP ÜLKER,Yuksel Hasan,ÖZCAN Gizem,topal erdem,Can Demet,Korkmaz Pervin,Çaltepe Gönül,KILIÇ Mehmet,Ozdogan Sebnem,CAKIR Erkan,ÇOBANOGLU NAZAN,PEKCAN SEVGI,CINEL GUZIN,ÖZÇELİK UĞUR,Dogru Deniz Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. Turkish Journal of Pediatrics, vol.65, no.2, 2023, ss.257 - 268. 10.24953/turkjped.2021.4930
AMA	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. Turkish Journal of Pediatrics. 2023; 65(2): 257 - 268. 10.24953/turkjped.2021.4930
Vancouver	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data. Turkish Journal of Pediatrics. 2023; 65(2): 257 - 268. 10.24953/turkjped.2021.4930
IEEE	Onay Z,Sismanlar Eyuboglu T,Aslan A,Ramasli Gursoy T,Yalcin E,Kiper N,Emiralioglu N,Selimoğlu Şen H,ŞEN v,ünal G,YILMAZ A,Kilinc A,cokugras H,Kilic Baskan A,Yazan H,Çollak A,Uzuner S,Sasihuseyinoglu A,ÖZCAN D,Altintas D,Kartal Öztürk G,Demir E,Bingöl A,BAŞARAN E,Cekic S,Sapan N,Irmak I,Damadoglu E,Tuğcu G,Eryilmaz Polat S,Özdemir A,harmancı k,KILIÇ G,Hangul M,Kose M,TAMAY Z,Yuksel H,ÖZCAN G,topal e,Can D,Korkmaz P,Çaltepe G,KILIÇ M,Ozdogan S,CAKIR E,ÇOBANOGLU N,PEKCAN S,CINEL G,ÖZÇELİK U,Dogru D "Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data." Turkish Journal of Pediatrics, 65, ss.257 - 268, 2023. 10.24953/turkjped.2021.4930
ISNAD	Onay, Zeynep Reyhan vd. "Clinical characteristics of patients requiring lung transplantation referral in national cystic fibrosis registry data". Turkish Journal of Pediatrics 65/2 (2023), 257-268. https://doi.org/10.24953/turkjped.2021.4930