Yıl: 2012 Cilt: 21 Sayı: 2 Sayfa Aralığı: 80 - 83 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Isolated left pulmonary artery agenesis: A case report

Öz:
Kardiyovasküler malformasyon olmaksızın unilateral pulmoner arter agenezisi nadir bir anomalidir. Biz izole sol pulmoner arter agenezisi olan bir hastanın goruntuleme bulgularını sunuyoruz. Yirmi yedi yaşındaki kadın hasta 5 yıldır süren nefes darlığı şikayetiyle hastanemize başvurdu. Akciğer grafisinde hafifçe küçük bir sol pulmoner hilus ve sol akciğer vardı. Kliniğimize pulmoner arter patolojisi şüphesi ile gönderildi. Sintigrafide normal ventilasyon ile birlikte sol akciğerde aperfüzyon izlendi. MDCT anjiografi sol pulmoner arter yokluğu ile birlikte sol hemitoraksta sistemik kollateraller gösterdi. Pulmoner arter agenezisi yetişkin yaşa kadar asemptomatik ve izole olabilir. Hem akciğer sintigrafisi hem de BT anjiografi bulguları ile birlikte bildirilen pulmoner arter agenezi hastası literatürde nadirdir. Akciğer ventilasyon-perfüzyon sintigrafisi, pulmoner emboli dışında, pulmoner arter ve dallarına ait diğer patolojileri aydınlatmada da kullanılabilir. (MIRT 2012;21:80-83)
Anahtar Kelime:

Konular: Radyoloji, Nükleer Tıp, Tıbbi Görüntüleme

İzole sol pulmoner arter agenezisi: Bir olgu sunumu

Öz:
Unilateral pulmonary artery agenesis without any cardiovascular malformation is a rare anomaly. We present the imaging findings of a patient who was diagnosed as isolated left pulmonary artery agenesis. A 27-year-old female patient was admitted to our hospital due to dyspnea during exercise for five years. Chest X-ray revealed minimally small left pulmonary hilum and left lung. She was admitted to our clinic with the suspicion of pulmonary artery pathology. Absent perfusion of the left lung with normal ventilation was visualized on scintigraphy. MDCT angiography of pulmonary arteries showed absent left main pulmonary artery with systemic collaterals around left hemithorax. Pulmonary artery agenesis can be asymptomatic and isolated until adulthood. Both scintigraphy and CT angiography images of pulmonary artery agenesis of a patient are rare in the literature. Pulmonary ventilationperfusion scintigraphy can be used not only for pulmonary embolism but also pathologies involving pulmonary artery and its branches. (MIRT 2012;21:80-83)
Anahtar Kelime:

Konular: Radyoloji, Nükleer Tıp, Tıbbi Görüntüleme
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
  • 1. Toews WH, Pappas G. Surgical management of absent right pulmonary artery with associated pulmonary hypertension. Chest 1983;84:497-499.
  • 2. Gluck MC, Moser KM. Pulmonary artery agenesis diagnosis with ventilation and perfusion scintiphotography. Circulation. 1970;41:859-867.
  • 3. Wyman SM. Congenital absence of pulmonary artery: its demonstration by roentgenography. Radiology 1954;62:321- 328.
  • 4. Cogswell TL, Singh S. Agenesis of the left pulmonary artery as a cause of hemoptysis. Angiology 1986;37:154-159.
  • 5. Werber J, Ramilo JL, London R, Harris VJ. Unilateral absence of a pulmonary artery. Chest 1983;84:729-732.
  • 6. Borgeson E, Vogel JH. Congenital unilateral absence of the left pulmonary artery. Echocardiography in reverse. Chest 1980;77:106-107.
  • 7. Gordon I, Helms P. Investigating the small lung: which imaging procedure? Arch Dis Child 1982;57:696-701.
  • 8. Ten Harkel AD, Blom NA, Ottenkamp J. Isolated unilateral absence of a pulmonary artery: A case report and review of the literature. Chest 2002;122:1471-1477.
  • 9. Prasad SK, Soukias N, Hornung T, Khan M, Pennell DJ, Gatzoulis MA, Mohiaddin RH. Role of magnetic resonance angiography in the diagnosis of major aortopulmonary collateral arteries and partial anomalous venous drainage. Circulation 2004;109:207- 214.
  • 10. Di Guglielmo L, Dore R, Vespro V. Pulmonary hypertension: role of computed tomography and magnetic resonance imaging. Ital Heart J 2005;6:846-851.
  • 11. Harris KM, Lloyd DC, Morrissey B, Adams H. The computed tomographic appearances in pulmonary artery atresia. Clin Radiol 1992;45:382-386.
  • 12. Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest 1995;108:670–676.
  • 13. Rupprecht E, Wunderlich P, Dietzsch HJ, Hennig K, Platzbecker H, Berger G, Leupold W, Wünsche W. Unilateral aplasia and hypoplasia of pulmonary artery in childhood (author's transl). Z Erkr Atmungsorgane 1977;147:57-72.
  • 14. Galuska L, Márton H. Absence of unilateral pulmonary circulation, detected by perfusion scintigraphy of the lung, and its clinical significance. Orv Hetil 1996;137:411-414.
  • 15. Schmid L, Lauer O, Langhammer H, Rupp N, Schlehe H, Pabst HW. Unilateral pulmonary artery aplasia with special reference to lung scintigraphy (author's transl). Nuklearmedizin 1979;18:226-231.
  • 16. Krall WR, Ploy-Song-Sang Y. Unilateral pulmonary artery aplasia presenting with chest pain and pleural effusion. South Med J 1980;73:233-236.
  • 17. Hentrich F, Stoermer J, Wiesemann G. Unilateral proximal aplasia of the pulmonary artery--studies on the clinical significance and embryologic interpretation. Klin Padiatr 1984;196:311-314.
  • 18. Wu MT, Pan HB, Chiang AA, Hsu HK, Chang HC, Peng NJ, Lai PH, Liang HL, Yang CF. Prediction of postoperative lung function in patients with lung cancer; comparison of quantitative CT with perfusion scintigraphy. AJR Am J Roentgenol 2002;178:667-672.
  • 19. Arriero JM, Gil J, Martín C, Mainar V, Romero S. Unilateral absence of a pulmonary artery: congenital disease or embolic occlusion? Eur Respir J 1991;4:1299–1300.
  • 20. Pickhardt PJ, Fischer KC. Unilateral hypoperfusion or absent perfusion on pulmonary scintigraphy: differential diagnosis. AJR Am J Roentgenol 1998;171:145-150.
APA BALCI T, Koç Z, KIRKIL G, POYRAZ A (2012). Isolated left pulmonary artery agenesis: A case report. , 80 - 83.
Chicago BALCI Tansel Ansal,Koç Zehra Pınar,KIRKIL Gamze,POYRAZ AHMET KURSAD Isolated left pulmonary artery agenesis: A case report. (2012): 80 - 83.
MLA BALCI Tansel Ansal,Koç Zehra Pınar,KIRKIL Gamze,POYRAZ AHMET KURSAD Isolated left pulmonary artery agenesis: A case report. , 2012, ss.80 - 83.
AMA BALCI T,Koç Z,KIRKIL G,POYRAZ A Isolated left pulmonary artery agenesis: A case report. . 2012; 80 - 83.
Vancouver BALCI T,Koç Z,KIRKIL G,POYRAZ A Isolated left pulmonary artery agenesis: A case report. . 2012; 80 - 83.
IEEE BALCI T,Koç Z,KIRKIL G,POYRAZ A "Isolated left pulmonary artery agenesis: A case report." , ss.80 - 83, 2012.
ISNAD BALCI, Tansel Ansal vd. "Isolated left pulmonary artery agenesis: A case report". (2012), 80-83.
APA BALCI T, Koç Z, KIRKIL G, POYRAZ A (2012). Isolated left pulmonary artery agenesis: A case report. Molecular Imaging and Radionuclide Therapy, 21(2), 80 - 83.
Chicago BALCI Tansel Ansal,Koç Zehra Pınar,KIRKIL Gamze,POYRAZ AHMET KURSAD Isolated left pulmonary artery agenesis: A case report. Molecular Imaging and Radionuclide Therapy 21, no.2 (2012): 80 - 83.
MLA BALCI Tansel Ansal,Koç Zehra Pınar,KIRKIL Gamze,POYRAZ AHMET KURSAD Isolated left pulmonary artery agenesis: A case report. Molecular Imaging and Radionuclide Therapy, vol.21, no.2, 2012, ss.80 - 83.
AMA BALCI T,Koç Z,KIRKIL G,POYRAZ A Isolated left pulmonary artery agenesis: A case report. Molecular Imaging and Radionuclide Therapy. 2012; 21(2): 80 - 83.
Vancouver BALCI T,Koç Z,KIRKIL G,POYRAZ A Isolated left pulmonary artery agenesis: A case report. Molecular Imaging and Radionuclide Therapy. 2012; 21(2): 80 - 83.
IEEE BALCI T,Koç Z,KIRKIL G,POYRAZ A "Isolated left pulmonary artery agenesis: A case report." Molecular Imaging and Radionuclide Therapy, 21, ss.80 - 83, 2012.
ISNAD BALCI, Tansel Ansal vd. "Isolated left pulmonary artery agenesis: A case report". Molecular Imaging and Radionuclide Therapy 21/2 (2012), 80-83.