Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood

KARA, F. Nazlı; ATAKAN, Canan; ÖZALP, Sıla; ÇAKAR, Nilgün; GOKDEMIR, Mahmut; Ensari, Arzu; DOĞANCI, Tümay

Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood

Tümay DOĞANCI, (Ankara Üniversitesi, Tıp Fakültesi, Pediatrik Gastroenteroloji Bilim Dalı, Ankara, Türkiye)

F. Nazlı KARA, (Girilmedi)

Mahmut GÖKDEMİR, (Girilmedi)

Arzu ENSARİ, (Girilmedi)

Sıla ÖZALP, (Girilmedi)

Nilgün ÇAKAR, (Girilmedi)

Canan ATAKAN (Girilmedi)

Turkish Journal of Gastroenterology

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Yıl: 2001 Cilt: 12 Sayı: 1 Sayfa Aralığı: 75 - 78 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood

Öz:

Anamnez ve klinik bulgularla birlikte tekrarlanan jejunal biyopsilerle teyid edilmiş primer intestinal lenfanjiektazi olgusu sunulmaktadır. Yüksek proteinli, orta zincir trigliserid eklenmiş, düşük yağ içeren diyetle hipoproteinemi ve kronik diyare başarılı bir şekilde tedavi edilmiştir. Olgumuzda klinikden bağımsız olarak ayrıca sol böbrek küçüklüğü ve aynı tarafta dilate üreter saptanmıştır. Bu olgu ender görüldüğü için yayınlanmaktadır

Anahtar Kelime: Biyopsi İshal Böbrek hastalıkları Üreter Çocuk Bağırsak hastalıkları

Konular: Cerrahi

Primer intestinal lenfanjiektazi: Çocukluk çağında ender görülen kronik diyare nedeni

Öz:

A case of primary intestinal lymphangiectasia which was diagnosed on the basis of multiple peroral jejunal biopsies along with a highly suggestive clinical history is presented. Treatment with a high-protein, very low fat diet with medium-chain triglycerides was effective in alleviating the diarrhea and hypoproteinemia. The patient also had a smaller than normal left kidney and a dilated ureter on the same side. This case is reported due to its rarity.

Anahtar Kelime: Child Intestinal Diseases Biopsy Diarrhea Kidney Diseases Ureter

Konular: Cerrahi

Belge Türü: Makale Makale Türü: Diğer Erişim Türü: Erişime Açık

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APA	DOĞANCI T, KARA F, GOKDEMIR M, Ensari A, ÖZALP S, ÇAKAR N, ATAKAN C (2001). Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. , 75 - 78.
Chicago	DOĞANCI Tümay,KARA F. Nazlı,GOKDEMIR Mahmut,Ensari Arzu,ÖZALP Sıla,ÇAKAR Nilgün,ATAKAN Canan Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. (2001): 75 - 78.
MLA	DOĞANCI Tümay,KARA F. Nazlı,GOKDEMIR Mahmut,Ensari Arzu,ÖZALP Sıla,ÇAKAR Nilgün,ATAKAN Canan Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. , 2001, ss.75 - 78.
AMA	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. . 2001; 75 - 78.
Vancouver	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. . 2001; 75 - 78.
IEEE	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C "Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood." , ss.75 - 78, 2001.
ISNAD	DOĞANCI, Tümay vd. "Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood". (2001), 75-78.

APA	DOĞANCI T, KARA F, GOKDEMIR M, Ensari A, ÖZALP S, ÇAKAR N, ATAKAN C (2001). Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. Turkish Journal of Gastroenterology, 12(1), 75 - 78.
Chicago	DOĞANCI Tümay,KARA F. Nazlı,GOKDEMIR Mahmut,Ensari Arzu,ÖZALP Sıla,ÇAKAR Nilgün,ATAKAN Canan Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. Turkish Journal of Gastroenterology 12, no.1 (2001): 75 - 78.
MLA	DOĞANCI Tümay,KARA F. Nazlı,GOKDEMIR Mahmut,Ensari Arzu,ÖZALP Sıla,ÇAKAR Nilgün,ATAKAN Canan Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. Turkish Journal of Gastroenterology, vol.12, no.1, 2001, ss.75 - 78.
AMA	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. Turkish Journal of Gastroenterology. 2001; 12(1): 75 - 78.
Vancouver	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood. Turkish Journal of Gastroenterology. 2001; 12(1): 75 - 78.
IEEE	DOĞANCI T,KARA F,GOKDEMIR M,Ensari A,ÖZALP S,ÇAKAR N,ATAKAN C "Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood." Turkish Journal of Gastroenterology, 12, ss.75 - 78, 2001.
ISNAD	DOĞANCI, Tümay vd. "Primary intestinal lymphangiectasia: A rare cause of chronic diarrhea in childhood". Turkish Journal of Gastroenterology 12/1 (2001), 75-78.