Gingival Rhabdomyosarcoma in an Adult: A Unique Entity

NAYAK, Meghanand T.; SIMGHVI, Abhishek; SAHNİ, Priya; DEORA, Shakti Singh

Gingival Rhabdomyosarcoma in an Adult: A Unique Entity

Priya SAHNİ, (Vyas Dental College & Hospital, Jodhpur, Rajasthan, INDIA)

Abhishek SIMGHVI, (Vyas Dental College & Hospital, Jodhpur, Rajasthan, INDIA)

Meghanand T. NAYAK, (Vyas Dental College & Hospital, Jodhpur, Rajasthan, INDIA)

Shakti Singh DEORA (Mathura Das Mathur Hospital, Jodhpur, Rajasthan, INDIA)

Türk Patoloji Dergisi

2 0

Yıl: 2015 Cilt: 31 Sayı: 2 Sayfa Aralığı: 153 - 157 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Gingival Rhabdomyosarcoma in an Adult: A Unique Entity

Öz:

Esas olarak çocukluk çağının malign bir tümörü olan rabdomyosarkom olgularının yaklaşık %40ı baş boyun bölgesinde lokalize olmakla birlikte oral kavitede nadirdir. Bu makalede, 36 yaşındaki erkek hastada mandibuler gingival yerleşimli embriyonel rabdomyosarkom olgusu sunulmuştur. Oral kavitede sınırları belirgin olmayan ve orta hattı geçen radyolusen kitle izlendi. Öyküsünden 6 ay önce aynı bölgeden benzer bir lezyonun eksize edildiği öğrenildi. Biyopsinin embriyonel rabdomyosarkom olarak raporlanmasını takiben en-blok rezeksiyon ve ardından kemoterapi ve radyoterapi uygulandı. Erişkin rabdomyosarkomlarının tekrarlama oranı yüksek olduğu için multimodal tedavi planı gereklidir. Makalede, rabdomyosarkomun klinik, radyolojik, histopatolojik bulguları ve tedavi yaklaşımı tartışılmıştır.

Anahtar Kelime:

Konular: Cerrahi

Bir Erişkin Dişeti Rabdomyosarkomu: Özgün Bir Antite

Öz:

Rhabdomyosarcoma is a disease that predominantly affects children. Approximately 40 per cent are located in the head and neck region but it is rare in the oral cavity. This article describes an interesting case of an embryonal rhabdomyosarcoma in a 36-year-old male, involving the mandibular gingiva. The lesion showed radiolucency with ill-defined margins that was crossing the midline. The history revealed a similar lesion six months back at the same site and the lesion had been completely excised. The biopsy reports confirmed the diagnosis of embryonal rhabdomyosarcoma after which en-bloc resection of the tumor was performed with administration of chemotherapy and radiotherapy. Due to high recurrence rate of rhabdomyosarcomas in adults, multimodal therapy should be planned for proper care of the patient. Clinical, radiological, histopathological and management aspects are discussed here.

Anahtar Kelime:

Konular: Cerrahi

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

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APA	SAHNİ P, SIMGHVI A, NAYAK M, DEORA S (2015). Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. , 153 - 157.
Chicago	SAHNİ Priya,SIMGHVI Abhishek,NAYAK Meghanand T.,DEORA Shakti Singh Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. (2015): 153 - 157.
MLA	SAHNİ Priya,SIMGHVI Abhishek,NAYAK Meghanand T.,DEORA Shakti Singh Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. , 2015, ss.153 - 157.
AMA	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. . 2015; 153 - 157.
Vancouver	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. . 2015; 153 - 157.
IEEE	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S "Gingival Rhabdomyosarcoma in an Adult: A Unique Entity." , ss.153 - 157, 2015.
ISNAD	SAHNİ, Priya vd. "Gingival Rhabdomyosarcoma in an Adult: A Unique Entity". (2015), 153-157.

APA	SAHNİ P, SIMGHVI A, NAYAK M, DEORA S (2015). Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. Türk Patoloji Dergisi, 31(2), 153 - 157.
Chicago	SAHNİ Priya,SIMGHVI Abhishek,NAYAK Meghanand T.,DEORA Shakti Singh Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. Türk Patoloji Dergisi 31, no.2 (2015): 153 - 157.
MLA	SAHNİ Priya,SIMGHVI Abhishek,NAYAK Meghanand T.,DEORA Shakti Singh Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. Türk Patoloji Dergisi, vol.31, no.2, 2015, ss.153 - 157.
AMA	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. Türk Patoloji Dergisi. 2015; 31(2): 153 - 157.
Vancouver	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S Gingival Rhabdomyosarcoma in an Adult: A Unique Entity. Türk Patoloji Dergisi. 2015; 31(2): 153 - 157.
IEEE	SAHNİ P,SIMGHVI A,NAYAK M,DEORA S "Gingival Rhabdomyosarcoma in an Adult: A Unique Entity." Türk Patoloji Dergisi, 31, ss.153 - 157, 2015.
ISNAD	SAHNİ, Priya vd. "Gingival Rhabdomyosarcoma in an Adult: A Unique Entity". Türk Patoloji Dergisi 31/2 (2015), 153-157.