Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri

Ajila, Vidya; NAİR, Mithula; Hegde, Shruthi; BABU, G Subhas; GHOSH, Rumela

Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri

Mithula NAİR, (Department of Oral Medicine and Radiology A. B Shetty Memorial Institute of Dental Sciences, Nitte University, India)

Vidya AJİLA, (Department of Oral Medicine and Radiology A. B Shetty Memorial Institute of Dental Sciences, Nitte University, India)

Shruthi HEGDE, (Department of Oral Medicine and Radiology A. B Shetty Memorial Institute of Dental Sciences, Nitte University, India)

G Subhas BABU, (Department of Oral Medicine and Radiology A. B Shetty Memorial Institute of Dental Sciences, Nitte University, India)

Rumela GHOSH (Department of Oral Medicine and Radiology A. B Shetty Memorial Institute of Dental Sciences, Nitte University, India)

Journal of Istanbul University Faculty of Dentistry

52 2

Yıl: 2017 Cilt: 51 Sayı: 3 Sayfa Aralığı: 45 - 49 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri

Öz:

Parry-Romberg sendromu ya da progresif hemifasiyal atrofi; yüz bölgesinde kas, kemik ve cilt dokusunda genellikle tek taraflı olarak görülen, yavaş ve progresif atrofi ile karakterize bir klinik tablodur. Normal ve anormal dokular arasındaki belirgin çizgiye kılıç darbesine benzetilerek "coup de sabre" adı verilmiştir. Yüz deformitesinin ciddiyeti hastalığın ortaya çıktığı yaşa göre değişir. Bu hastalarda kozmetik tedavi başlıca seçenek olmasına karşılık yüz gelişimi tamamlanıncaya kadar ertelenmelidir. Bu olgu bildirisinde 10 aylıkken progresif hemifasiyal atrofi teşhisi koyulan 43 yaşındaki bir kadın hasta sunulmuştur. Sendromun erken yaşta başlamasına ve neredeyse yüzün sağ yarısının tamamını etkilemesine rağmen hastada gözlerle ilgili bir bulguya ya da dişlerle ilgili bir gelişim bozukluğuna rastlanmamıştır

Anahtar Kelime:

Konular: Diş Hekimliği

CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME

Öz:

Parry-Romberg syndrome or progressive hemifacial atrophy is a craniofacial disorder characterized by slow and progressive atrophy, generally unilateral, of facial tissues including muscles, bones and skin. The coup de sabre is a clear line of demarcation seen between the normal and abnormal structures. The severity of the facial deformity is dependent on the age of onset of the disease. Cosmetic management is the only available treatment and has to be delayed until facial growth is completed. The present case report deals with a 43-year-old woman with progressive hemifacial atrophy which started from the age of 10 months. Despite almost complete involvement of the right paramedian area and the early age of onset, she had neither eye changes nor any dental malformations

Anahtar Kelime:

Konular: Diş Hekimliği

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	NAİR M, Ajila V, Hegde S, BABU G, GHOSH R (2017). Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. , 45 - 49.
Chicago	NAİR Mithula,Ajila Vidya,Hegde Shruthi,BABU G Subhas,GHOSH Rumela Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. (2017): 45 - 49.
MLA	NAİR Mithula,Ajila Vidya,Hegde Shruthi,BABU G Subhas,GHOSH Rumela Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. , 2017, ss.45 - 49.
AMA	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. . 2017; 45 - 49.
Vancouver	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. . 2017; 45 - 49.
IEEE	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R "Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri." , ss.45 - 49, 2017.
ISNAD	NAİR, Mithula vd. "Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri". (2017), 45-49.

APA	NAİR M, Ajila V, Hegde S, BABU G, GHOSH R (2017). Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. Journal of Istanbul University Faculty of Dentistry, 51(3), 45 - 49.
Chicago	NAİR Mithula,Ajila Vidya,Hegde Shruthi,BABU G Subhas,GHOSH Rumela Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. Journal of Istanbul University Faculty of Dentistry 51, no.3 (2017): 45 - 49.
MLA	NAİR Mithula,Ajila Vidya,Hegde Shruthi,BABU G Subhas,GHOSH Rumela Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. Journal of Istanbul University Faculty of Dentistry, vol.51, no.3, 2017, ss.45 - 49.
AMA	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. Journal of Istanbul University Faculty of Dentistry. 2017; 51(3): 45 - 49.
Vancouver	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri. Journal of Istanbul University Faculty of Dentistry. 2017; 51(3): 45 - 49.
IEEE	NAİR M,Ajila V,Hegde S,BABU G,GHOSH R "Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri." Journal of Istanbul University Faculty of Dentistry, 51, ss.45 - 49, 2017.
ISNAD	NAİR, Mithula vd. "Parry-Romberg Sendromunun Klinik ve Radyografik Özellikleri". Journal of Istanbul University Faculty of Dentistry 51/3 (2017), 45-49.