Renal Primitive Neuroectodermal Tumor
Yıl: 2017 Cilt: 4 Sayı: 2 Sayfa Aralığı: 82 - 84 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022
Renal Primitive Neuroectodermal Tumor
Öz: Böbreğin primitif nöroektodermal tümörleri (PNET) oldukça nadir görülen ve ileri derecede malign neoplazilerdir. Genellikle çocuk ve genç erişkinlerde görülür. Biz 19 yaşında sol yan ağrısı ile kliniğimize başvuran bir kadın hastayı sunduk. Ultrasonografi sol böbrekte kitle tespit etti. Bilgisayarlı tomografisinde sol tarafta 10x8 cm boyutlarında heterojen, nekrotik alanlar içeren kitle görüldü. Hastaya radikal nefrektomi ve lenfadenektomi yapıldı. İmmünohistokimyasal olarak CD99 ve FL-1 ile pozitif boyandı. Mikroskobik ve immünohistokimyasal olarak PNET tanısı konuldu. Sonrasında hastaya 8 kür kemoterapi verildi, şu ana kadarki 6 aylık takibinde metastaz izlenmedi. Renal PNET nadir görülen ve kötü prognozlu bir tümördür, bazen Ewing sarkom ile ayrımı güç olmaktadır. Özellikle çocuklarda ve genç erişkinlerde renal tümörlerin ayırıcı tanısında PNET düşünülmelidir. Bu olgu sunumu ile tümör hakkında bir farkındalık oluşturulması amaçlanmıştır
Anahtar Kelime: Böbrek Primitif Nöroektodermal Tümörü
Öz: Renal primitive neuroectodermal tumor (PNET) is a rare entity and highly malignant neoplasm. It generally occurs in young adults and children. We report a case of 19-year-old female with the complaint of left flank pain. Ultrasonography showed a tumor of the left kidney. A big left inhomogeneous renal mass of 10x8 cm with areas of necrosis was observed on computed tomography. The patient underwent radical nephrectomy with lymphadenectomy. Immunohistochemical stains were positive for CD99 and FL-1. Immunohistochemical and microscopic results were compatible with PNET. Furthermore, the patient received eight cycles of chemotherapy, and was still alive without metastases at 6-month followup. Renal PNET is a rare and poor prognosis tumor. It is sometimes difficult to discriminate between PNET and Ewing’s sarcoma. Renal PNET must be included in the differential diagnosis of renal tumors particularly in young adults and children. With this case report it aimed to create awareness about PNET
Anahtar Kelime: Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık
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| APA | ÇELIK H, ÇAMTOSUN A, DURSUN İ, AKPOLAT N, YILDIRIM İ (2017). Renal Primitive Neuroectodermal Tumor. , 82 - 84. |
| Chicago | ÇELIK HÜSEYIN,ÇAMTOSUN Ahmet,DURSUN İbrahim,AKPOLAT NUSRET,YILDIRIM İsmail Okan Renal Primitive Neuroectodermal Tumor. (2017): 82 - 84. |
| MLA | ÇELIK HÜSEYIN,ÇAMTOSUN Ahmet,DURSUN İbrahim,AKPOLAT NUSRET,YILDIRIM İsmail Okan Renal Primitive Neuroectodermal Tumor. , 2017, ss.82 - 84. |
| AMA | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ Renal Primitive Neuroectodermal Tumor. . 2017; 82 - 84. |
| Vancouver | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ Renal Primitive Neuroectodermal Tumor. . 2017; 82 - 84. |
| IEEE | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ "Renal Primitive Neuroectodermal Tumor." , ss.82 - 84, 2017. |
| ISNAD | ÇELIK, HÜSEYIN vd. "Renal Primitive Neuroectodermal Tumor". (2017), 82-84. |
| APA | ÇELIK H, ÇAMTOSUN A, DURSUN İ, AKPOLAT N, YILDIRIM İ (2017). Renal Primitive Neuroectodermal Tumor. Journal of Urological Surgery, 4(2), 82 - 84. |
| Chicago | ÇELIK HÜSEYIN,ÇAMTOSUN Ahmet,DURSUN İbrahim,AKPOLAT NUSRET,YILDIRIM İsmail Okan Renal Primitive Neuroectodermal Tumor. Journal of Urological Surgery 4, no.2 (2017): 82 - 84. |
| MLA | ÇELIK HÜSEYIN,ÇAMTOSUN Ahmet,DURSUN İbrahim,AKPOLAT NUSRET,YILDIRIM İsmail Okan Renal Primitive Neuroectodermal Tumor. Journal of Urological Surgery, vol.4, no.2, 2017, ss.82 - 84. |
| AMA | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ Renal Primitive Neuroectodermal Tumor. Journal of Urological Surgery. 2017; 4(2): 82 - 84. |
| Vancouver | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ Renal Primitive Neuroectodermal Tumor. Journal of Urological Surgery. 2017; 4(2): 82 - 84. |
| IEEE | ÇELIK H,ÇAMTOSUN A,DURSUN İ,AKPOLAT N,YILDIRIM İ "Renal Primitive Neuroectodermal Tumor." Journal of Urological Surgery, 4, ss.82 - 84, 2017. |
| ISNAD | ÇELIK, HÜSEYIN vd. "Renal Primitive Neuroectodermal Tumor". Journal of Urological Surgery 4/2 (2017), 82-84. |
