Yıl: 2018 Cilt: 27 Sayı: 3 Sayfa Aralığı: 158 - 162 Metin Dili: İngilizce DOI: 10.5336/pediatr.2018-60083

A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis

Öz:
A 17-year old girl admitted to our outpatient unit with hoarseness and shortness ofbreath. Her physical examination showed nasal deformity. Her medical history included the diagnosis of uveitis and type 1 diabetes mellitus (DM) as well as asthma and chronic sinusitis. Diagnostic work-up showed involvement of the upper respiratory tract (saddle nose deformity, chronicsinusitis), laryngo-tracheo-bronchial involvement (subglottic and bronchial stenosis) and pulmonary involvement (pulmonary nodules) leading to a diagnosis of granulomatous polyangiitis(GPA). We report this child on the basis of the fact that coexistence of type 1 DM and GPA hasnever been reported in our country previously.
Anahtar Kelime:

Konular:
Fen > Tıp > Pediatri

Tip 1 Diabetes Mellitus ve ANCA-Negatif Granülomatozisli Polianjitis Birlikteliği Olan Olgu

Öz:
On yedi yaşında kız hasta, ses kısıklığı ve nefes darlığı şikayetiyle polikliniğimize başvurdu. Fizik muayenesinde burun deformitesi olan olgunun geçmiş hikayesinden üveit ve tip I diabetes mellitus tanısının olduğu, astım ve kronik sinüzit tanılarıyla tedaviler aldığı fakat solunum semptomlarının düzelmediği öğrenildi. Fizik muayene ve tetkiklerinde üst solunum yolu tutulumu (semer burun defekti, kronik sinüzit), larengo-trakeobronkial tutulum (subglottik ve bronkial stenoz) ve akciğer tutulumu (pulmoner nodül) tespit edilerek olguya granülomatozisli polianjitis tanısı konuldu. Tip I diabetes mellitus ve granülomatozisli polianjitis birlikteliği ülkemizden daha önce bildirilmemiş olup ilk olması açısından önemlidir.
Anahtar Kelime:

Konular:
Fen > Tıp > Pediatri
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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APA BAŞARAN A, ÖZ L, AKYOL S, ÜNAL Ö, ÇOMAK E, KOYUN M, BİNGÖL A (2018). A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis. Türkiye Klinikleri Pediatri Dergisi, 27(3), 158 - 162. 10.5336/pediatr.2018-60083
Chicago BAŞARAN Abdurrahman,ÖZ Latife,AKYOL Seçil,ÜNAL Ömer,ÇOMAK Elif,KOYUN Mustafa,BİNGÖL Ayşen A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis. Türkiye Klinikleri Pediatri Dergisi 27, no.3 (2018): 158 - 162. 10.5336/pediatr.2018-60083
MLA BAŞARAN Abdurrahman,ÖZ Latife,AKYOL Seçil,ÜNAL Ömer,ÇOMAK Elif,KOYUN Mustafa,BİNGÖL Ayşen A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis. Türkiye Klinikleri Pediatri Dergisi, vol.27, no.3, 2018, ss.158 - 162. 10.5336/pediatr.2018-60083
AMA BAŞARAN A,ÖZ L,AKYOL S,ÜNAL Ö,ÇOMAK E,KOYUN M,BİNGÖL A A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis. Türkiye Klinikleri Pediatri Dergisi. 2018; 27(3): 158 - 162. 10.5336/pediatr.2018-60083
Vancouver BAŞARAN A,ÖZ L,AKYOL S,ÜNAL Ö,ÇOMAK E,KOYUN M,BİNGÖL A A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis. Türkiye Klinikleri Pediatri Dergisi. 2018; 27(3): 158 - 162. 10.5336/pediatr.2018-60083
IEEE BAŞARAN A,ÖZ L,AKYOL S,ÜNAL Ö,ÇOMAK E,KOYUN M,BİNGÖL A "A Patient with Coexistent Type 1 Diabetes Mellitus and ANCA-Negative Granulomatosis with Polyangiitis." Türkiye Klinikleri Pediatri Dergisi, 27, ss.158 - 162, 2018. 10.5336/pediatr.2018-60083