Grisel’s syndrome is nontraumatic atlantoaxial subluxation secondary to inflammatory conditions or surgery in the head and neckregion due to anomalous head posture. In this case report, a 6-year-old female patient, diagnosed as Grisel’s syndrome following the surgery for the repair of cleft palate with velopharyngeal insufficiency is presented. This is to note the importance of perioperative positioning and postoperative stabilization. 6 years old female child, with a weight of 23 kg admitted to the hospital for speech disorders and velopharyngeal insufficiency associated with cleft palate. She underwent surgery for the repair of cleft palate and three weeks after surgery, she was readmitted to the hospital with abnormal head posture, pain and limitation in neck movements. After cervical CT scanning, atlantoaxial subluxation was confirmed. She was diagnosed as Grisel’s syndrome and treated with conservative therapy by stabilization of the neck with a hard cervical collar and medical treatment. Extreme head positions are sometimes necessary for cleft lip and palate surgeries. Early diagnosis of Grisel’s syndrome is critical for a successful treatment.