Introduction: Cardiac involvement is rare in hydatid cystdisease, which accounted for 0.5%-2% of all hydatidosis cases.Cardiac cysts usually occur as part of a wider infestation withextracardiac involvement. This study aimed to describe thegeneral characteristics, imaging findings, and range of organinvolvement in cases of cardiac hydatid disease.Methods: Retrospective assessment of cardiac hydatid diseaserecords, between 2007 and 2019, was undertaken to identifypatients with cardiac hydatidosis. Hydatid cysts were assessedby transthoracic echocardiography, magnetic resonanceimaging, and computed tomography. Clinical symptoms,treatment modalities, and follow-up were also evaluated.Results: Over the study period, 22 (13 males: 59.1%; meanage: 43.1 years; range: 12-63 years) patients with 24 cardiachydatid cysts were identified. The most common symptomwas chest pain, which occurred in 13 (59.1%) patients. Cardiaccysts were located in the left ventricle (n=10, 41.7%), rightventricle (n=5, 20.8%), interventricular septum (n=5, 20.8%),and pericardium (n=4, 16.7%). Extracardiac involvement waspresent in 14 (63.6%) patients, most commonly affecting theliver (n=10, 45.4%), but in 8 (36.3%) patients, there was noextracardiac organ involvement. Cardiac hydatid cysts weresurgically removed in 20 (90.9%) patients.Conclusion: Cardiac hydatid disease is very uncommon, withthe left ventricle as the most commonly affected structure in thisseries. Chest pain was the most common presenting symptom.Extracardiac involvement is common, so patients with cardiachydatid cysts should be investigated for involvement of otherorgans.