Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia

Objective: To retrospectively evaluate the follow-up data in patients with 46,XX congenital adrenal hyperplasia (CAH) who were raisedmale.Methods: A national database was created. The data of patients were asked to be recorded in the data form.Results: The median (range) age of diagnosis was three (0.1-18.3) years in 44 patients. Twenty nine cases were diagnosed after the ageof two years. Most (95.4%) cases were stage 4-5 virilized. Hysterectomy and bilateral salpingoopherectomy, at a median age of 7.25(2.4-25.3) years, was performed in 35 cases. Testicular prostheses were placed in 11 (25%) cases at a median age of 11.2 (2.8-17) years.The median final height was 149.2 (132.8-172) cms in 38 patients, including simple virilizing (n=18), salt-wasting (n=6), and 11-betahydroxylase (n=12). Of the 16 patients above the age of eighteen, university education was completed in 25%.Conclusion: It was seen that most (65.9%) of the 46,XX CAH cases raised male were diagnosed after two years of age. In these cases,hysterectomy and bilateral salpingoopherectomy, genital corrective surgeries and testicular prosthesis operations were performed in avery wide age rage.

Anahtar Kelime:

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

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APA	SAVAS ERDEVE S, aycan z, Çetinkaya S, Öztürk A, Bas F, Poyrazoglu S, Darendeliler F, Özsu E, siklar z, demiral m, unal e, Ozbek M, gürbüz f, yuksel b, Evliyaoğlu O, akyurek n, berberoglu m (2021). Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. , 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
Chicago	SAVAS ERDEVE SENAY,aycan zehra,Çetinkaya Semra,Öztürk Ayşe Pınar,Bas Firdevs,Poyrazoglu Sukran,Darendeliler Feyza,Özsu Elif,siklar zeynep,demiral meliha,unal edip,Ozbek Mehmet Nuri,gürbüz fatih,yuksel bilgin,Evliyaoğlu Olcay,akyurek nesibe,berberoglu merih Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. (2021): 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
MLA	SAVAS ERDEVE SENAY,aycan zehra,Çetinkaya Semra,Öztürk Ayşe Pınar,Bas Firdevs,Poyrazoglu Sukran,Darendeliler Feyza,Özsu Elif,siklar zeynep,demiral meliha,unal edip,Ozbek Mehmet Nuri,gürbüz fatih,yuksel bilgin,Evliyaoğlu Olcay,akyurek nesibe,berberoglu merih Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. , 2021, ss.180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
AMA	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. . 2021; 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
Vancouver	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. . 2021; 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
IEEE	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m "Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia." , ss.180 - 186, 2021. 10.4274/jcrpe.galenos.2020.2020.0216
ISNAD	SAVAS ERDEVE, SENAY vd. "Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia". (2021), 180-186. https://doi.org/10.4274/jcrpe.galenos.2020.2020.0216

APA	SAVAS ERDEVE S, aycan z, Çetinkaya S, Öztürk A, Bas F, Poyrazoglu S, Darendeliler F, Özsu E, siklar z, demiral m, unal e, Ozbek M, gürbüz f, yuksel b, Evliyaoğlu O, akyurek n, berberoglu m (2021). Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. Journal of Clinical Research in Pediatric Endocrinology, 13(2), 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
Chicago	SAVAS ERDEVE SENAY,aycan zehra,Çetinkaya Semra,Öztürk Ayşe Pınar,Bas Firdevs,Poyrazoglu Sukran,Darendeliler Feyza,Özsu Elif,siklar zeynep,demiral meliha,unal edip,Ozbek Mehmet Nuri,gürbüz fatih,yuksel bilgin,Evliyaoğlu Olcay,akyurek nesibe,berberoglu merih Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. Journal of Clinical Research in Pediatric Endocrinology 13, no.2 (2021): 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
MLA	SAVAS ERDEVE SENAY,aycan zehra,Çetinkaya Semra,Öztürk Ayşe Pınar,Bas Firdevs,Poyrazoglu Sukran,Darendeliler Feyza,Özsu Elif,siklar zeynep,demiral meliha,unal edip,Ozbek Mehmet Nuri,gürbüz fatih,yuksel bilgin,Evliyaoğlu Olcay,akyurek nesibe,berberoglu merih Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. Journal of Clinical Research in Pediatric Endocrinology, vol.13, no.2, 2021, ss.180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
AMA	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. Journal of Clinical Research in Pediatric Endocrinology. 2021; 13(2): 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
Vancouver	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia. Journal of Clinical Research in Pediatric Endocrinology. 2021; 13(2): 180 - 186. 10.4274/jcrpe.galenos.2020.2020.0216
IEEE	SAVAS ERDEVE S,aycan z,Çetinkaya S,Öztürk A,Bas F,Poyrazoglu S,Darendeliler F,Özsu E,siklar z,demiral m,unal e,Ozbek M,gürbüz f,yuksel b,Evliyaoğlu O,akyurek n,berberoglu m "Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia." Journal of Clinical Research in Pediatric Endocrinology, 13, ss.180 - 186, 2021. 10.4274/jcrpe.galenos.2020.2020.0216
ISNAD	SAVAS ERDEVE, SENAY vd. "Clinical Characteristics of 46,XX Males with Congenital Adrenal Hyperplasia". Journal of Clinical Research in Pediatric Endocrinology 13/2 (2021), 180-186. https://doi.org/10.4274/jcrpe.galenos.2020.2020.0216