Background: Fulminant hepatic failure (FHF) may be a rare presentation of autoimmune hepatitis (AIH) in previously as ymptomatic adolescents. Celiac disease (CD) is a chronic immune disease that may be associated with severe forms of liverdisease and coexists with AIH. We report a patient presenting with an FHF at the diagnosis of AIH and CD. Case Report: An 8-year-old female patient who had no known background or family history of liver disease was referred toour center with an FHF diagnosis. Her clinical and laboratory findings fulfilled the criteria of seronegative AIH and CD. After7 days of starting the medical treatment, encephalopathy and liver function tests gradually improved. Conclusion: AIH and CD usually follow a chronic course and rarely coexist. However, they should be considered the etiol ogies of FHF and should be treated promptly.