An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia

GUNGOR, IBRAHIM LEVENT; BAYRAK, Oytun; SARICA, Murat; ONAR, Musa; TÜRKER, Hande

An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia

Hande TÜRKER, (Ondokuz Mayıs Üniversitesi, Tıp Fakültesi, Nöroloji Anabilim Dalı, Samsun, Türkiye)

Oytun BAYRAK, (Ondokuz Mayıs Üniversitesi, Tıp Fakültesi, Nöroloji Anabilim Dalı, Samsun, Türkiye)

Levent GÜNGÖR, (Ondokuz Mayıs Üniversitesi, Tıp Fakültesi, Nöroloji Anabilim Dalı, Samsun, Türkiye)

Murat SARICA, (Ondokuz Mayıs Üniversitesi, Tıp Fakültesi, Nöroloji Anabilim Dalı, Samsun, Türkiye)

Musa ONAR (Ondokuz Mayıs Üniversitesi, Tıp Fakültesi, Nöroloji Anabilim Dalı, Samsun, Türkiye)

Marmara Medical Journal

11 0

Yıl: 2006 Cilt: 19 Sayı: 3 Sayfa Aralığı: 139 - 144 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia

Öz:

Multifokal motor nöropati (MMN), kalıcı iletim bloklarının eşlik ettiği, ilerleyici, asimetrik ekstremite güçsüzlüğüyle karakterizedir. Duysal etkilenim çok seyrek olarak görülür. MMN'nin kranial sinir tutulumu ve refleks artışı ile birlikteliği nadiren bildirilmiştir. Burada, el kaslarındaki ilerleyici güçsüzlüğe, orbikularis okuli kaslarında güçsüzlük ve dilde fasikülasyonun eşlik ettiği 32 yaşında MMN'li bir kadın hasta sunulmuştur. Elektrofizyolojik incelemede her iki ulnar, sağ median ve sol posterior tibial sinirlerde iletim blokları ve F dalgalarında persistans anormalliği saptandı. Bu bulgularla birlikte, ileti bloklarının persistansı ve tablonun İVİG'e yanıtlı olması bize multifokal motor nöropati tanısını düşündürttü. Hasta, kliniğindeki seyrek rastlanır öğeler nedeniyle rapor edilmeye değer bulundu.

Anahtar Kelime:

Konular: Genel ve Dahili Tıp

Kranial sinir tutulumu ve hiperrefleksi ile giden multifokal motor nöropati: Olgu sunumu

Öz:

Multifocal motor neuropathy is characterized by progressive, asymmetric weakness of the limbs with persistent conduction blocks (CB). Sensory loss is very rare and it also rarely presents with cranial nerve involvement and hyperreflexia. Here we described a 32-year-old woman with progressive weakness of hand muscles associated with weakness of orbicularis oculi muscles and fasciculations of tongue. The electrophysiological examination revealed persistent conduction blocks in both of the ulnar, right median and left posterior tibial nerves together with F-waves with abnormal persistence. These findings and the persistency of conduction blocks along with a response to IVIG made it likely that the diagnosis was multifocal motor neuropathy. The case seemed to be worth reporting because of her unusual clinical findings.

Anahtar Kelime:

Konular: Genel ve Dahili Tıp

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	TÜRKER H, BAYRAK O, GUNGOR I, SARICA M, ONAR M (2006). An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. , 139 - 144.
Chicago	TÜRKER Hande,BAYRAK Oytun,GUNGOR IBRAHIM LEVENT,SARICA Murat,ONAR Musa An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. (2006): 139 - 144.
MLA	TÜRKER Hande,BAYRAK Oytun,GUNGOR IBRAHIM LEVENT,SARICA Murat,ONAR Musa An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. , 2006, ss.139 - 144.
AMA	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. . 2006; 139 - 144.
Vancouver	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. . 2006; 139 - 144.
IEEE	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M "An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia." , ss.139 - 144, 2006.
ISNAD	TÜRKER, Hande vd. "An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia". (2006), 139-144.

APA	TÜRKER H, BAYRAK O, GUNGOR I, SARICA M, ONAR M (2006). An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. Marmara Medical Journal, 19(3), 139 - 144.
Chicago	TÜRKER Hande,BAYRAK Oytun,GUNGOR IBRAHIM LEVENT,SARICA Murat,ONAR Musa An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. Marmara Medical Journal 19, no.3 (2006): 139 - 144.
MLA	TÜRKER Hande,BAYRAK Oytun,GUNGOR IBRAHIM LEVENT,SARICA Murat,ONAR Musa An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. Marmara Medical Journal, vol.19, no.3, 2006, ss.139 - 144.
AMA	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. Marmara Medical Journal. 2006; 19(3): 139 - 144.
Vancouver	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia. Marmara Medical Journal. 2006; 19(3): 139 - 144.
IEEE	TÜRKER H,BAYRAK O,GUNGOR I,SARICA M,ONAR M "An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia." Marmara Medical Journal, 19, ss.139 - 144, 2006.
ISNAD	TÜRKER, Hande vd. "An unusual case of multifocal motor neuropathy with cranial nerve involvement and hyperreflexia". Marmara Medical Journal 19/3 (2006), 139-144.