Yıl: 2000 Cilt: 34 Sayı: 3 Sayfa Aralığı: 329 - 332 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Poland sendromu

Öz:
Poland sendromu herediter olmayan ve nedeni bilinmeyen konjenital bir anomalidir. Klinik görünümü değişkendir. Bu sendromda pektoralis majör kas yokluğu, aynı tarafta sıklıkla brakisindaktili ve üst ekstremite hipoplazi vardır. Bu çalışmada pektoralis majör kas yokluğuyla birlikte kol, önkol ve elde hipoplazi, brakisindaktili, orta falankslarda hipoplazi ve/veya aplazi bulunan iki olgu sunuldu. Her iki olguda kozmetik görünümde bozukluk ve el fonksiyonlarında azalma vardı. Olgulardan birine sindaktili açılması için cerrahi tedavi uygulandı. Cerrahi tedavi sonrası kozmetik görümde kısmen düzelme ve el fonksiyonel kapasitesinde artma oldu. İkinci olgu önerilen ameliyatı kabul etmedi.
Anahtar Kelime: Cerrahi işlemler, operatif Sindaktili Pektoralis kasları Olgu sunumu Anomaliler Kol Poland sendromu Konjenital anomali

Konular: Genel ve Dahili Tıp

Poland's syndrome

Öz:
Poland's syndrome is a congenital anomaly that is not hereditary and is of unknown origin. Clinical features are variable and includes the absence of the pectoralis major and minor, upper extremity abnormalities, and often synbrachydactyly. The arm and more frequently the forearm are hypoplastic. We report two cases presenting with the absence of the pectoralis major and minor, hypoplasia of the upper extremity, and synbrachydactyly. Poor cosmetic appearance and low functional capacity, particularly in hand functions were the main complaints. One patient underwent surgery for the release of syndactyly, which resulted in improved functional capacity and cosmetic appearance. The latter patient refused surgery.
Anahtar Kelime: Arm Poland Syndrome Congenital anomaly Surgical Procedures, Operative Syndactyly Pectoralis Muscles Case report Abnormalities

Konular: Genel ve Dahili Tıp
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Bibliyografik
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APA ARSLAN H, NECMİOĞLU S, ÇOBAN H (2000). Poland sendromu. , 329 - 332.
Chicago ARSLAN Hüseyin,NECMİOĞLU Serdar,ÇOBAN Hüseyin Poland sendromu. (2000): 329 - 332.
MLA ARSLAN Hüseyin,NECMİOĞLU Serdar,ÇOBAN Hüseyin Poland sendromu. , 2000, ss.329 - 332.
AMA ARSLAN H,NECMİOĞLU S,ÇOBAN H Poland sendromu. . 2000; 329 - 332.
Vancouver ARSLAN H,NECMİOĞLU S,ÇOBAN H Poland sendromu. . 2000; 329 - 332.
IEEE ARSLAN H,NECMİOĞLU S,ÇOBAN H "Poland sendromu." , ss.329 - 332, 2000.
ISNAD ARSLAN, Hüseyin vd. "Poland sendromu". (2000), 329-332.
APA ARSLAN H, NECMİOĞLU S, ÇOBAN H (2000). Poland sendromu. Acta Orthopaedica et Traumatologica Turcica, 34(3), 329 - 332.
Chicago ARSLAN Hüseyin,NECMİOĞLU Serdar,ÇOBAN Hüseyin Poland sendromu. Acta Orthopaedica et Traumatologica Turcica 34, no.3 (2000): 329 - 332.
MLA ARSLAN Hüseyin,NECMİOĞLU Serdar,ÇOBAN Hüseyin Poland sendromu. Acta Orthopaedica et Traumatologica Turcica, vol.34, no.3, 2000, ss.329 - 332.
AMA ARSLAN H,NECMİOĞLU S,ÇOBAN H Poland sendromu. Acta Orthopaedica et Traumatologica Turcica. 2000; 34(3): 329 - 332.
Vancouver ARSLAN H,NECMİOĞLU S,ÇOBAN H Poland sendromu. Acta Orthopaedica et Traumatologica Turcica. 2000; 34(3): 329 - 332.
IEEE ARSLAN H,NECMİOĞLU S,ÇOBAN H "Poland sendromu." Acta Orthopaedica et Traumatologica Turcica, 34, ss.329 - 332, 2000.
ISNAD ARSLAN, Hüseyin vd. "Poland sendromu". Acta Orthopaedica et Traumatologica Turcica 34/3 (2000), 329-332.